Corticobasal Syndrome (CBS) - Phenomenology Atlas
Video 6.1 (C6c1): Corticobasal Syndrome with Cortical Sensory Loss
Left-hand action myoclonus, impaired graphesthesia and stereognosis, and focal right perirolandic cortical atrophy.
Video 6.2 (C6c2): Corticobasal Syndrome with Limb Apraxia
Loss of proprioceptive control and impaired individuated finger movements of the left hand with reduced arm swing.
Video 6.3 (C6c3): Corticobasal Syndrome with Ideomotor Apraxia
Left-hand dexterity impairment, body-part-as-object substitution, and progressive hemispatial neglect.
Video 6.4 (C6c7): Corticobasal Syndrome with Apraxia and Cognitive Dysfunction
Ideomotor apraxia, impaired dexterity, head-thrust saccades, reduced arm swing, and inability to copy pentagons.
Video 6.5 (C6c12): Corticobasal Syndrome with Cortical Myoclonus
Left-arm myoclonus, athetosis, rigidity, cortical sensory loss, and stimulus-sensitive cortical reflex myoclonus.
Video 6.6 (C6c16): Advanced Corticobasal Syndrome
Continuous left-arm myoclonus, severe limb apraxia, rigidity, cortical sensory deficits, and gait impairment.
Video 6.7 (C6c17): Corticobasal Syndrome with Dystonic Pistol-Grip Hand
Severe right-arm rigidity, dystonic hand posturing, gait hesitation, and asymmetric parkinsonism.
Video 6.8 (C6c18): Cortical Reflex Myoclonus
Action- and position-induced myoclonus with stimulus-sensitive cortical reflex myoclonus and preserved parkinsonism-free examination.
Video 6.9 (C6c20): Corticobasal Syndrome with Fixed Limb Dystonia
Severe right-arm dystonia, apraxia, absent arm swing, and preserved gait.
Video 6.10 (C6c21): Corticobasal Syndrome with Cortical Sensory Loss
Marked right-sided rigidity, impaired stereognosis, foot dystonia, and severe gait dysfunction.
Video 6.11 (C6c22): Asymmetric Corticobasal Syndrome
Profound right-hand bradykinesia and loss of individuated finger movements with preserved language and sensation.
Video 6.12 (C6c23): Corticobasal Syndrome with Severe Limb Apraxia
Left-arm dystonia, ideomotor apraxia, rigidity, and marked gait impairment.
Video 6.13 (C6c24): Corticobasal Syndrome with Myoclonic Tremor
Asymmetric parkinsonism, action-induced myoclonus mimicking tremor, and prominent apraxia.
Video 6.14 (C6c25): Corticobasal Syndrome with Alien Limb Features
Severe left-limb apraxia, cortical sensory loss, involuntary limb elevation, and gait dysfunction.
Video 6.15 (C6c28): Corticobasal Syndrome with Hemispatial Neglect
Profound left-hand dysfunction, astereognosis, visuospatial neglect, and evolution toward alien limb syndrome.
Video 6.16 (C6c29): Corticobasal Syndrome with Mirror Movements
Bilateral cortical reflex myoclonus, oculomotor apraxia, severe left-arm apraxia, and mirror movements.
Video 6.17 (C6c30): Behavioral-Speech Variant Tauopathy
Aprosodic speech, mild asymmetric parkinsonism, emotional indifference, and frontotemporal metabolic deficits.
Video 6.18 (C6c32): Primary Progressive Aprosodia
Markedly abnormal speech prosody with minimal parkinsonian findings and preserved gait.
Video 6.19 (C6c33): Tauopathy Speech Syndrome
Isolated motoric, aprosodic speech with otherwise normal neurological examination.
Video 6.20 (C6c34): Progressive Aprosodic Speech Disorder
Severely impaired speech prosody with minimal bradykinesia and preserved mobility.
Video 6.21 (C6c35): Nonfluent Primary Progressive Aphasia with Parkinsonism
Aprosodic speech, word-finding difficulty, mild asymmetric parkinsonism, and left frontotemporal atrophy.
Video 6.22 (C6c36): Progressive Aphasia Syndrome
Expressive-receptive aphasia with paraphasic errors, preserved reading, and mild bradykinesia.
Video 6.23 (C6c37): Nonfluent Aphasia with Asymmetric Parkinsonism
Halting speech, impaired speech repetition, left-hand motor impairment, and preserved comprehension.
Video 6.24 (C6c38): Parkinsonian Nonfluent Aphasia
Limited speech output, rigidity, bradykinesia, and mild gait impairment without apraxia.
Video 6.25 (C6c39): Severe Nonfluent Primary Progressive Aphasia
Single-syllable perseverative speech, inability to repeat, preserved calculation ability, and normal gait.
Video 6.26 (C6c40): Aphasia with Apraxia and Asymmetric Parkinsonism
Language impairment, inability to imitate learned actions, right-sided rigidity, and dystonic hand posturing.
Video 6.27 (C6c41): Progressive Apraxia Syndrome
Severe bilateral limb apraxia and agraphia with preserved speech, gait, and strength.
-Pending
Video 6.28 (C6c42): Isolated Ideomotor Apraxia Syndrome
Profound bilateral hand apraxia with normal language, cognition, gait, and postural control.
-Pending
