Article type: Pictures in Neurology
Article
title: Neurofibromatosis two presenting with
bilateral sixth and seventh nerve palsies
Journal: Neurology and Clinical
Neuroscience
Year: 2019
Authors:
Jamir Pitton Rissardo, Ana LetÃcia Fornari Caprara
E-mail:
jamirrissardo@gmail.com
ABSTRACT
A 25-year-old female was admitted with weakness of
facial muscles and binocular horizontal diplopia within 3h of onset. She was
previously healthy and her family history was remarkable for brain tumors. The
neurological examination showed the weakness of bilateral upper and lower
facial muscles associated with bilateral lateral rectus muscle palsy.
Laboratory tests were within normal limits. A noncontrast cranial computed
tomography (CT) scan was suggestive of tumors in the posterior cranial fossa; a
contrast CT scan revealed the lesions. Prednisone 60 mg/day was
started. Upon further questioning, the patient reported that on the maternal
side of the family, there were three relatives, including her mother, who had a
diagnosis of neurofibromatosis 2 (NF2). On the seventh admission day, she was
referred to the neurosurgical service of another city.
Keywords: Abducens nerve, facial nerve, neurofibromatosis, neurofibromatosis 2, paralysis
Full text available at:
DOI
Citation
Rissardo JP, Caprara AL. Neurofibromatosis
two presenting with bilateral sixth and seventh nerve palsies. Neurol Clin
Neurosci 2019;7:47
Figure 1. Neuroimages showing bilateral lesion with extension into the meatus, heterogeneous contrast enhancement, and obliteration of the respective pontocerebellar angles associated with brainstem compression in the posterior cranial fossa (indicated by the arrow). In addition, adjacent bone remodeling with smooth corticated edges can be observed. Axial(A), sagittal(B), and coronal(C) views of contrast CT.