Definition
Idiopathic chronic intracranial vascular steno-occlusive disease characterized by progressive stenosis of the terminal segments of the internal carotid arteries bilaterally and/or partial stenosis or occlusion of the proximal portions of the anterior cerebral arteries and the middle cerebral arteries and formation of an abnormal network of vessels at the base of the skull
Causes
- idiopathic
- SCD association
Findings
Classification
- Suzuki
Puff of smoke sign
