Chorea Phenomenology Atlas (Part 4): Autoimmune, Metabolic and Structural Chorea

Chorea Phenomenology Atlas (Part 4): Autoimmune, Metabolic and Structural Chorea

Autoimmune and Inflammatory Choreas

Video 11.37 (C11c54): Anti-Cardiolipin Antibody Hemichorea
Severe right hemichorea resolving completely after immunotherapy.

Video 11.38 (C11c55): Anti-Cardiolipin Antibody Chorea
Mild generalized chorea associated with autoimmune disease.

Video 11.39 (C11c56): Crohn Disease-Associated Chorea
Generalized chorea responsive to tetrabenazine.

Video 11.40 (C11c57): Anti-Thyroglobulin Antibody Chorea
Moderate generalized chorea with marked activation by concentration.

Sydenham Chorea

Video 11.41 (C11c58–59): Sydenham Chorea
Childhood generalized chorea with hypotonia, milkmaid grip, and gait impairment.

Video 11.42 (C11c60): Mild Sydenham Chorea
Generalized chorea, emotional lability, and impaired balance.

Autoimmune Encephalitis

Video 11.43 (C11c61): LGI1 Antibody-Associated Chorea
Asymmetric chorea resolving after corticosteroid treatment.

Video 11.44 (C11c62): NMDA Receptor Encephalitis with Orofacial Dyskinesias
Classic oral-facial stereotypies and encephalopathic state.

Video 11.45 (C11c63): NMDA Receptor Encephalitis
Repetitive hand stereotypies in a cognitively preserved child.

Structural Chorea and Hemichorea

Video 11.46 (C11c64): Structural Hemichorea-Hemidystonia
Left hemi-chorea with dystonia, hypotonia, and ataxia.

Video 11.48 (C11c66): Structural Chorea after Pontine Hemorrhage
Mixed tremor, dystonia, and choreiform finger movements with brainstem ocular findings.

Hemiballism

Video 11.47 (C11c65): Acute Vascular Hemiballism
Violent right-sided ballistic movements due to acute stroke.

Video 11.49 (C11c67): Severe Hemiballism
Extremely violent right-sided ballistic movements requiring padding and high-dose tetrabenazine.

Video 11.50 (C11c68): Left Hemiballism with Chorea
Proximal and distal ballistic movements with milkmaid grip.

Video 11.51 (C11c69): Subthalamic Nucleus Hemiballism
Classic hemiballism due to hemorrhagic STN lesion.

Hyperglycemic Chorea/Ballism

Video 11.52 (C11c70): Nonketotic Hyperglycemia Hemiballism
Severe unilateral ballistic movements improving after glucose control and haloperidol.


Video 11.53 (C11c71): Hyperglycemic Generalized Chorea
Diffuse chorea markedly improved after metabolic correction.

Other Acquired Choreas

Video 11.54 (C11c72): Post-Pump Chorea
Mild generalized chorea following cardiopulmonary bypass.

Video 11.55 (C11c73): Biballism from Cerebral Toxoplasmosis
Generalized ballistic movements evolving into persistent hemichorea after treatment.

Video 11.56 (C11c74): Choreoathetoid Cerebral Palsy
Severe hemichorea and ballistic limb movements causing major functional impairment.