Unusual Movement Disorders (Part 1): Athetosis, Myokymia, Myorhythmia and Oculogyric Crisis

Unusual Movement Disorders (Part 1): Athetosis, Myokymia, Myorhythmia and Oculogyric Crisis

Video 14.1 (C14c1): Dyskinetic Cerebral Palsy with Athetosis
Generalized choreoathetosis, dystonic hand posturing (Hammond’s hand), dysarthria, and impaired dexterous movements.

Video 14.2 (C14c2): Sensory Athetosis after Guillain-Barré Syndrome
Right-arm athetosis due to profound proprioceptive loss, with pseudoathetotic movements and dorsal column injury.

Video 14.3 (C14c3): Sensory Athetosis
Pseudoathetosis with dystonic hand posturing and impaired joint position sense, worsening when visual guidance is removed.

Video 14.4 (C14c4): Friedreich Ataxia with Athetosis
Severe upper-limb athetosis with sensory neuropathy, pes cavus, and areflexia.

Video 14.5 (C14c5): Idiopathic Myokymia
Worm-like undulating contractions of intrinsic foot muscles.

Video 14.6 (C14c6): Facial Myokymia from Pontine Glioma
Continuous unilateral facial myokymia associated with facial weakness and abducens palsy.

Video 14.7 (C14c7): Focal Facial Myokymia
Task-induced focal lower lip contraction with superimposed myokymia.

Video 14.8 (C14c8): Gelsolin Amyloidosis with Facial Myokymia
Periocular and facial myokymia triggered by sustained eye closure and smiling.

Video 14.9 (C14c9): Oculomasticatory and Limb Myorhythmia in Whipple Disease
Synchronous rhythmic eye, jaw, and limb movements characteristic of Whipple disease.

Video 14.10 (C14c10): Smile Tremor
Rapid oscillatory facial tremor triggered by sustained smiling.

Video 14.11 (C14c11): Bilateral Smile Tremor
Symmetric facial quivering induced by smiling.

Video 14.12 (C14c12): Oculogyric Crisis in Vascular Parkinsonism
Acute oculogyric crisis with autonomic activation, myoclonus, and parkinsonism.

Video 14.13 (C14c13): Oculogyric Crisis in Parkinson's Disease
Classic oculogyric crisis with retrocollis, dystonic posturing, and painful forced gaze deviation.

Video 14.14 (C14c14): Oculogyric Crisis in DYT-12 Dystonia
Recurrent dystonic eye deviation and posturing markedly improved by levodopa.

Video 14.15 (C14c15): Tetrabenazine-Induced Oculogyric Crisis
Drug-induced tonic upgaze, retrocollis, and dystonic posturing.