Myoclonus Phenomenology Atlas (Part 1): Cortical, Reflex and Post-Hypoxic Myoclonus

Myoclonus Phenomenology Atlas (Part 1): Cortical, Reflex and Post-Hypoxic Myoclonus

Video 10.1 (C10c1): Rasmussen Encephalitis with Epilepsia Partialis Continua
Continuous focal facial seizures with left hemiparesis and rhythmic athetotic arm movements.
- Pending

Video 10.2 (C10c2): Cortical Myoclonus in Corticobasal Syndrome
Action- and position-induced left-hand myoclonus with severe impairment of individuated finger movements.

Video 10.3 (C10c3): Advanced Cortical Myoclonus in Corticobasal Syndrome
Frequent left-arm myoclonic jerks coalescing into near-continuous myoclonic volleys.

Video 10.4 (C10c4): Alzheimer's Disease with Cortical Myoclonus
Cognitive impairment and stimulus/action-induced torso and upper-limb myoclonus.

Video 10.5 (C10c5): Lance-Adams Syndrome (Posthypoxic Myoclonus)
Action and negative myoclonus severely impairing coordination, pouring, and gait.

Video 10.6 (C10c6): Postanoxic Action Myoclonus
Asymmetric action myoclonus affecting handwriting, eating, and pouring tasks.

Video 10.7 (C10c7): Familial Cortical Tremor/Myoclonus with Orthostatic Symptoms
Standing-induced leg myoclonus relieved by walking or light touch.

Video 10.8 (C10c8): Familial Cortical Tremor/Myoclonus Syndrome
Combined cortical myoclonus and essential-tremor-like oscillatory tremor responsive to levetiracetam and primidone.

Video 10.9 (C10c9): Thalamic Asterixis
Left-arm negative myoclonus and action myoclonus following a right thalamic infarction.

Video 10.10 (C10c10): Hereditary Hyperekplexia (Infant)
Exaggerated non-habituating startle responses and Moro reflex responsive to clonazepam.

Video 10.11 (C10c11): Hyperekplexia Animal Model
Poll-Hereford cattle demonstrating hereditary startle disease.

Video 10.12 (C10c12): Severe Reticular Reflex Myoclonus
Devastating posthypoxic proximal and truncal myoclonus causing complete functional dependence.

Video 10.13 (C10c13): Posthypoxic Myoclonus Treated with GPi DBS
Action and negative myoclonus markedly improved after deep brain stimulation.