Faciobrachial dystonic seizure!
Overlap of epilepsy & movement disorders
Sarosh R. Irani
First to mention FBDS w/ LGI1
2) Definition
Sudden, brief, lateralized tonic contractions involving upper limb & ipsilateral face (less freq leg), often associated with hand dystonia
- unilateral, bilateral asynchronous, or alternat with a short delay (à bascule) and tend to recur several times day
3) Important
- prodrome of limbic encephalitis associated with Abs to the VGKCs (anti‐leucine‐rich glioma‐inactivated 1 [LGI1] encephalitis)
- clinical diagnosis (EEG only 34%)
- therapeutic window for immunotherapy (preventing sequels)
- good immunotherapy response
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29) Faciobrachio-crural dystonic seizures (FBCDS)
Involvement of the leg is rare, and little has been reported on so-called faciobrachio-crural dystonic seizures (FBCDS).